Hyperammonemia - 13 Studies Found
Recruiting |
: N-Carbamylglutamate (Carbaglu) In The Treatment Of Hyperammonemia : Inborn Errors of Metabolism : 2009-02-12 : Drug: N-carbamylglutamate 100 mg/kg/day or 2.2 g/M2/day in 3-4 divided doses for 3 days |
Recruiting |
: Blood Sugars in Children With Idiopathic Seizures. :
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Completed |
: Phase 2B Efficacy/Safety of Ornithine Phenylacetate in Hospitalized Cirrhotic Patients With Hepatic Encephalopathy (STOP-HE) :
: 2013-10-11 :
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Completed |
: Fat and Sugar Metabolism During Exercise, With and Without L-carnitine in Patients With Carnitine Transporter Deficiency : Carnitine Transporter, Plasma-membrane, Deficiency of : 2013-08-05 : Dietary Supplement: Break in L-carnitine treatment Levocarnitine oral tablet supplement at individual do |
Completed |
: Influence of OCTN2 Variants on Carnitine Status and Plasma Triglycerides : Carnitine Transporter Deficiency : 2005-09-14 : Other: Fasting blood and urine collection Not applicable no drugs dispensed |
Completed |
: Study of the Safety of HPN (Hyperion)-100 for the Long-Term Treatment of Urea Cycle Disorders (Treat UCD) : Urea Cycle Disorders : 2009-07-24 : Drug: HPN-100 HPN-100 is a triglyceride that has a similar mechanism of action as NaPBA. It is a liquid |
Completed |
: Efficacy and Safety of HPN-100 for the Treatment of Adults With Urea Cycle Disorders : Urea Cycle Disorders : 2009-10-08 :
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Completed |
: Investigation of Brain Nitrogen in Partial Ornithine Transcarbamylase Deficiency (OTCD) Using 1 H MRS, DTI, and fMRI : Ornithine Transcarbamylase Deficiency : 2012-03-30 :
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Completed |
: Study of the Safety, Pharmacokinetics and Efficacy of HPN-100, in Pediatric Subjects With Urea Cycle Disorders (UCDs) : Urea Cycle Disorders : 2011-04-29 : Drug: HPN-100 HPN-100 is a pro-drug of PAA that combines with glutamine to provide an alternative vehicl |
Completed |
: Study of the Safety and Tolerability of HPN-100 Compared to Sodium Phenylbutyrate in Children With Urea Cycle Disorders : Urea Cycle Disorders : 2009-07-24 :
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